✦ LIBER ✦

Stiff-man syndrome in a child

✍ Scribed by Caridad Garzo; Manuel Pérez-Sotelo; Alfredo Traba; Angel Esteban; Dr. Francisco Grandas; José Luis Muñoz-Blanco

Publisher: John Wiley and Sons
Year: 1998
Tongue: English
Weight: 347 KB
Volume: 13
Category: Article
ISSN: 0885-3185
DOI: 10.1002/mds.870130233

No coin nor oath required. For personal study only.

✦ Synopsis

broadens the considerable clinical heterogeneity of movement disorders reported in late-onset HD. tromyographic pattern of continuous muscle activity at rest in the affected muscles. Muscle spasms and axial stiffness usually improve with diazepam or baclofen.'

Since the initial description of SMS by Moersch and Wolt-

Legends to the Videotape

Segment 1. This segment of the videotape shows the patient sitting in a chair exhibiting paroxysmal involuntary belching and aerophagia with one episode of paroxysmal rotatory torticollis and upper limb myoclonus.

Segment 2. This segment demonstrates paroxysmal bilateral blepharospasm on attempted lateral gaze initiation.

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