alpha-1-antitrypsin; PiZZ, a1-ATZ phenotype; ER, endoplasmic acts with the target P 1 -P 1 residues of the reactive center loop, reticulum; MHC, major histocompatibility complex. the loop inserts further into the gap in the A sheet, generating From the: Departments of Pediatrics, Cell Biology, and
Pathogenesis of deficient serum α1-antitrypsin in the typeZZhomozygote
✍ Scribed by Peter T. Rowley; Maria Luz Sevilla; Robert H. Schwartz
- Publisher
- Springer
- Year
- 1974
- Tongue
- English
- Weight
- 429 KB
- Volume
- 12
- Category
- Article
- ISSN
- 0006-2928
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