Stored dolichyl pyrophosphoryl oligosacc
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Hall, Nicholas A. ;Thomas-Oates, Jane E. ;Dell, Anne ;Haltia, Matti ;Lake, Brian
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Article
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1992
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John Wiley and Sons
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English
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Each of the 3 childhood forms of Batten disease, juvenile (JB), late-infantile (LIB), and infantile (IB), have abnormally high brain concentrations of dolichyl pyrophosphoryl oligosaccharides (Dol-PP-0s). In this study, the carbohydrate portions of Dol-PP-OS were analysed: in J B and LIB, they range