𝔖 Bobbio Scriptorium
✦   LIBER   ✦

LIVER DISEASE AND α1-ANTITRYPSIN DEFICIENCY

✍ Scribed by Muensch, HelmutA.; Maslow, WilliamC.

Book ID
123122548
Publisher
The Lancet
Year
1982
Tongue
English
Weight
400 KB
Volume
320
Category
Article
ISSN
0140-6736

No coin nor oath required. For personal study only.

📜 SIMILAR VOLUMES

Molecular pathogenesis of liver disease
Molecular pathogenesis of liver disease in α1-antitrypsin deficiency
✍ J H Teckman; D Qu; D H Perlmutter 📂 Article 📅 1996 🏛 John Wiley and Sons 🌐 English ⚖ 320 KB

alpha-1-antitrypsin; PiZZ, a1-ATZ phenotype; ER, endoplasmic acts with the target P 1 -P 1 residues of the reactive center loop, reticulum; MHC, major histocompatibility complex. the loop inserts further into the gap in the A sheet, generating From the: Departments of Pediatrics, Cell Biology, and

Liver disease in children with pizz α1-a
Liver disease in children with pizz α1-antitrypsin deficiency
✍ Fayez K. Ghishan; Harry L. Greene 📂 Article 📅 1988 🏛 John Wiley and Sons 🌐 English ⚖ 446 KB

We present our experience with 18 pediatric patients with a,-antitrypsin deficiency of the PiZZ phenotype. Fifteen patients (83%) presented with neonatal cholestatic jaundice at a mean age of 2 f 0.6 months (2S.D.). The ma1e:female ratio was 15:3, indicating a male predominance. All metabolic, infec