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Liver Disease and Intermediate α1-Antitrypsin Deficiency

✍ Scribed by Eriksson, Sten

Book ID
114692596
Publisher
Wiley (Blackwell Publishing)
Year
2009
Weight
320 KB
Volume
210
Category
Article
ISSN
0001-6101

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We present our experience with 18 pediatric patients with a,-antitrypsin deficiency of the PiZZ phenotype. Fifteen patients (83%) presented with neonatal cholestatic jaundice at a mean age of 2 f 0.6 months (2S.D.). The ma1e:female ratio was 15:3, indicating a male predominance. All metabolic, infec