Domino liver transplantation for familia
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Hemming, Alan W. ;Cattral, Mark S. ;Chari, Ravi S. ;Greig, Paul D. ;Lilly, Lesli
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Article
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1998
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Wiley (John Wiley & Sons)
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English
β 64 KB
Familial amyloid polyneuropathy is an autosomal dominant disorder in which the liver produces a variant prealbumin that is deposited along nerves, leading to a progressive and fatal polyneuropathy that begins in the third decade of life. Liver transplantation has been the only successful treatment t