๐”– Bobbio Scriptorium
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Acute axonal neuropathy in maple syrup urine disease

โœ Scribed by Kleopas A. Kleopa; David M. Raizen; Christopher A. Friedrich; Mark J. Brown; Shawn J. Bird


Publisher
John Wiley and Sons
Year
2001
Tongue
English
Weight
126 KB
Volume
24
Category
Article
ISSN
0148-639X

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๐Ÿ“œ SIMILAR VOLUMES


Maple syrup urine disease
โœ Crome, L. ;Dutton, G. ;Ross, C. F. ๐Ÿ“‚ Article ๐Ÿ“… 1961 ๐Ÿ› Wiley (John Wiley & Sons) ๐ŸŒ English โš– 656 KB
Exchange transfusion in acute episodes o
โœ U. Wendel; U. Langenbeck; I. Lombeck; H. J. Bremer ๐Ÿ“‚ Article ๐Ÿ“… 1982 ๐Ÿ› Springer ๐ŸŒ English โš– 428 KB

Two neonates with maple syrup urine disease were treated by exchange transfusion. Within 15 h blood leucine and K/CA concentrations were lowered from 2.6raM to 1.1raM using 570 to 620ml blood per kg body weight. The other branched-chain amino acid/keto acid pairs fell to normal. During exchange tran

Leucine turnover in maple syrup urine di
โœ J. V. Leonard; A. M. Umpleby; E. M. Naughten; M. A. Boroujerdi; P. H. Sonksen ๐Ÿ“‚ Article ๐Ÿ“… 1983 ๐Ÿ› Springer ๐ŸŒ English โš– 231 KB
Maple syrup urine disease: Treatment of
โœ G. Hammersen; L. Wille; H. Schmidt; P. Lutz; H. Bickel ๐Ÿ“‚ Article ๐Ÿ“… 1978 ๐Ÿ› Springer ๐ŸŒ English โš– 530 KB

Three patients with maple syrup urine disease were treated during the acute neonatal stage. Multiple exchange transfusions proved to be a satisfactory means of achieving rapid clinical and biochemical improvement during this phase. On the other hand, evidence is provided suggesting that in addition

Domino liver transplantation in maple sy
โœ Ajai Khanna; Marquis Hart; William L. Nyhan; Tarek Hassanein; Janice Panyard-Dav ๐Ÿ“‚ Article ๐Ÿ“… 2006 ๐Ÿ› John Wiley and Sons ๐ŸŒ English โš– 290 KB

Liver transplantation has been reported in a few cases of maple syrup urine disease (MSUD), but is controversial. Many patients with approved indications for liver transplantation die before grafts are available. A 25-yr-old man with MSUD underwent liver transplantation, and his liver was used as a