Two neonates with maple syrup urine disease were treated by exchange transfusion. Within 15 h blood leucine and K/CA concentrations were lowered from 2.6raM to 1.1raM using 570 to 620ml blood per kg body weight. The other branched-chain amino acid/keto acid pairs fell to normal. During exchange tran
โฆ LIBER โฆ
Insulin to assist treatment of acute episodes in maple syrup urine disease
โ Scribed by U. Wendel; I. Lombeck; H. J. Bremer; U. Langenbeck
- Publisher
- Springer
- Year
- 1982
- Tongue
- English
- Weight
- 229 KB
- Volume
- 5
- Category
- Article
- ISSN
- 0141-8955
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