Leucine turnover in maple syrup urine disease
β Scribed by J. V. Leonard; A. M. Umpleby; E. M. Naughten; M. A. Boroujerdi; P. H. Sonksen
- Publisher
- Springer
- Year
- 1983
- Tongue
- English
- Weight
- 231 KB
- Volume
- 6
- Category
- Article
- ISSN
- 0141-8955
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Liver transplantation has been reported in a few cases of maple syrup urine disease (MSUD), but is controversial. Many patients with approved indications for liver transplantation die before grafts are available. A 25-yr-old man with MSUD underwent liver transplantation, and his liver was used as a
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