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Unusual nocturnal motor restlessness in a patient with spinocerebellar ataxia 3

✍ Scribed by Imad Ghorayeb; Federica Provini; Bernard Bioulac; François Tison

Publisher
John Wiley and Sons
Year
2005
Tongue
English
Weight
201 KB
Volume
20
Category
Article
ISSN
0885-3185

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✦ Synopsis

Abstract

Video‐polysomnographic monitoring of a female patient with spinocerebellar ataxia 3 (SCA‐3) in whom rapid eye movement (REM) sleep behavior disorder was clinically suspected demonstrated recurrent episodes of unusual nocturnal motor restlessness occurring during non‐REM sleep and severely disturbing both the patient and her bed partner's sleep. Even if nocturnal manifestations are common features of SCA‐3 and increasingly recognized, such a case has never been reported before. We discuss this peculiar movement disorder as a particular manifestation of the wide spectrum of parasomnias occurring in such a rare neurodegenerative disease. © 2005 Movement Disorder Society

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