Bilateral cystic adenomatoid malformation of the lung (CAML), solid type (Stocker 111), is a rare malformation that we observed sonographically in two fetuses at 23 weeks. The ultrasonic image showed an echogenic mass compressing the heart and occupying the whole thoracic cavity. Massive ascites, pr
Ultrasonic prenatal diagnosis of type III congenital cystic adenomatoid malformation of lung
β Scribed by Rajni V. Diwan; James N. Brennan; Elliott H. Philipson; Shail Jain; Errol M. Bellon
- Publisher
- John Wiley and Sons
- Year
- 1983
- Tongue
- English
- Weight
- 463 KB
- Volume
- 11
- Category
- Article
- ISSN
- 0091-2751
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β¦ Synopsis
Congenital cystic adenomatoid malformation (CCAM) of the lung is a rare benign disorder. Three types have been distinguished: cystic, intermediate, and solid,' or types I, 11, and 111, respectively.2 Type I11 lesions are the rarest; we found only six case^^-^ in an extensive review of the English literature. There is a male preponderance, without racial or geographic preference or any genetic predisposition.
There may be associated hydrops, with stillbirth or neonatal death. The invariably fatal outcome is related to the lack of early diagnosis and surgical treatment. With refinements in sonographic instrumentation and greater availability of antenatal examination, it may be possible to salvage these infants by surgical decompression in the immediate postnatal period. So far, only one case has been studied s~nographically.~ We report a second case and present criteria which may be useful in prenatal diagnosis.
CASE REPORT
A 25-yr-old gravida 1, para 0, woman was referred at 32 wk gestation with polyhydramnios. Ultrasonic examination revealed gross polyhydramnios, an abnormally thick, hydropic placenta, and a single male fetus in cephalic presentation. There was marked cutaneous edema and gross ascites. The left lung appeared voluminous, and the heart was displaced well over to the right From the Departments of Radiology,* Obstetrics and Gynecology,
π SIMILAR VOLUMES
## Abstract Prenatal identification of lung abnormalities has increased with prenatal surveillance. Treatment usually requires serial ultrasound observation but in rare situations in utero therapy may be required for fetal survival. We review the genetics, prenatal evaluation, and treatment of lung
Congenital cystic adenomatoid malformation (CCAM) of the lung is a rare pulmonary lesion, characterized by an excessive overgrowth of the terminal respiratory bronchioles.',' About 200 cases have been reported in the literature to date. The lesion is almost always unilateral3 and may occur in any lo