Congenital cystic adenomatoid malformation (CCAM) of the lung is a rare benign disorder. Three types have been distinguished: cystic, intermediate, and solid,' or types I, 11, and 111, respectively.2 Type I11 lesions are the rarest; we found only six case^^-^ in an extensive review of the English li
Prenatal diagnosis of bilateral cystic adenomatoid malformation of the lung
✍ Scribed by Andreas Rempen; Axel Feige; Peter Wünsch
- Publisher
- John Wiley and Sons
- Year
- 1987
- Tongue
- English
- Weight
- 630 KB
- Volume
- 15
- Category
- Article
- ISSN
- 0091-2751
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✦ Synopsis
Bilateral cystic adenomatoid malformation of the lung (CAML), solid type (Stocker 111), is a rare malformation that we observed sonographically in two fetuses at 23 weeks. The ultrasonic image showed an echogenic mass compressing the heart and occupying the whole thoracic cavity. Massive ascites, probably as a result of heart failure, was apparent. The prognosis is fatal. Prenatal diagnosis enables termination of pregnancy and saves the mother from invasive procedures in case of fetal distress. In unilateral, more favorable lesions, the managing physician is prepared for respiratory distress of the newborn and an emergency operation.
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## Abstract Prenatal identification of lung abnormalities has increased with prenatal surveillance. Treatment usually requires serial ultrasound observation but in rare situations in utero therapy may be required for fetal survival. We review the genetics, prenatal evaluation, and treatment of lung
Congenital cystic adenomatoid malformation (CCAM) of the lung is a rare pulmonary lesion, characterized by an excessive overgrowth of the terminal respiratory bronchioles.',' About 200 cases have been reported in the literature to date. The lesion is almost always unilateral3 and may occur in any lo
Neonatal survival of fetuses with space-occupying thoracic lesions is dependent upon the basic underlying disease, extent of involvement, and the presence or absence of other associated prenatal findings such as fetal hydrops, polyhydramnios, or displacement of the fetal heart, all accepted poor pro