Familial erythrophagocytic lymphohistioc
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Eva Gross-Kieselstein; Paulina Navon; D. Branski; A. Abrahamov; Lea Dollberg
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Article
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1981
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Springer
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English
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A 21/2-month-old infant suffering from pyrexia, purpura, hepatosplenomegaly, pancytopenia and hyperlipidemia is reported. Liver and spleen biopsies revealed mononuclear histiocytic infiltration with marked erythrophagocytosis. The girl died at 7I/2 months of age. Her brother died in infancy with an