Sickle cell disease is the most common inherited disorder in African-Americans. Although the primary defect is hematological, the changes in the erythrocytes lead to a vasculopathy with multiorgan injury. The pulmonary complications, i.e., acute chest syndrome and chronic sickle cell lung disease, a
The spine in sickle cell disease
โ Scribed by M. Sadat-Ali; A. Ammar; J. Ran Corea; A. W. Ibrahim
- Publisher
- Springer
- Year
- 1994
- Tongue
- English
- Weight
- 585 KB
- Volume
- 18
- Category
- Article
- ISSN
- 0341-2695
No coin nor oath required. For personal study only.
โฆ Synopsis
extrdmes de 4 it 28 ans. Des modifications structurales du corps vertdbral lides d l'hyperplasie mddullaire sont survenues chez 44% des patients. Des ndcroses avasculaires responsables d'un effondrement du corps vertebral ont dtd observdees chez 9 patients (26.5%). La spondylite infectieuse, qui constitue la complication la plus grave, a concerni 8 patients (23.5%), dont la plupart ont bdndfici~ d'une ddcompression antdrolatdrale et de greffes osseuses. Nous pensons que le rachis est souvent atteint au cours de la drdpanocytose et qu'un traitement agressif et une dtroite surveillance sont ndcessaires pour dviter des sdquelles majeures.
๐ SIMILAR VOLUMES
Sickle cell anemia and the related hemoglobinopathies are associated with a large spectrum of renal abnormalities. The patients have impaired urinary concentrating ability, defects in urinary acidification and potassium excretion, and supranormal proximal tubular function. The latter is manifest by