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Stimulation of Lipid Peroxidation in Vitro in Rat Brain by the Metabolites Accumulating in Maple Syrup Urine Disease

✍ Scribed by Fernanda U. Fontella; Edson Gassen; Vânia Pulrolnik; Clóvis M.D. Wannmacher; Adriane B. Klein; Moacir Wajner; Carlos S. Dutra-Filho

Book ID: 110326416
Publisher: Springer
Year: 2002
Tongue: English
Weight: 67 KB
Volume: 17
Category: Article
ISSN: 0885-7490
DOI: 10.1023/a:1014004414733

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## Abstract Severe neurological symptoms, cerebral edema, and atrophy are common features of the inherited metabolic disorder maple syrup urine disease (MSUD). However, the pathomechanisms involved in the neuropathology of this disease are not well established. In this study, we investigated the ef