Sjogren-Larsson syndrome
✍ Scribed by Meena Sood; Amita Trehan; J. Dinakaran; R K Marwaha
- Publisher
- Springer-Verlag
- Year
- 2002
- Tongue
- English
- Weight
- 212 KB
- Volume
- 69
- Category
- Article
- ISSN
- 0019-5456
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📜 SIMILAR VOLUMES
A family with 12 children, 6 of whom had Sjrgren-Larsson syndrome, was studied clinically. On CT, all six siblings with the disease had patchy regions of white matter hypodensity, most marked in the frontal lobes, which were confluent in the more severe cases. The ventricles were not enlarged and no
Cranial CT in a case of Sjögren-Larsson syndrome (SLS) showed a striking loss of attenuation of supratentorial white matter. This is in accordance with the myelin loss found at microscopic brain examination of patients with SLS, but not with the only report of five patients examined by cranial CT. T