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Cranial CT in the Sjogren-Larsson syndrome

✍ Scribed by L. J. M. M. Mulder; A. P. Oranje; M. C. B. Loonen

Publisher
Springer
Year
1987
Tongue
English
Weight
236 KB
Volume
29
Category
Article
ISSN
0028-3940

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✦ Synopsis

Cranial CT in a case of Sjögren-Larsson syndrome (SLS) showed a striking loss of attenuation of supratentorial white matter. This is in accordance with the myelin loss found at microscopic brain examination of patients with SLS, but not with the only report of five patients examined by cranial CT. The considerable myelin loss may be detected only by more recent generations of CT scanners and seems to be stationary during lifetime.

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