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Retinal oxidation, apoptosis and age- and sex-differences in the mnd mutant mouse, a model of neuronal ceroid lipofuscinosis

✍ Scribed by Rosetta Guarneri; Domenica Russo; Caterina Cascio; Stefania D'Agostino; Giacoma Galizzi; Paolo Bigini; Tiziana Mennini; Patrizia Guarneri

Book ID: 113499730
Publisher: Elsevier Science
Year: 2004
Tongue: English
Weight: 699 KB
Volume: 1014
Category: Article
ISSN: 0006-8993
DOI: 10.1016/j.brainres.2004.04.040

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## Abstract The neuronal ceroid lipofuscinoses (NCLs) are a family of devastating pediatric neurodegenerative disorders and currently represent the most common form of pediatric‐onset neurodegeneration. Infantile NCL (INCL), the most aggressive of these disorders, is caused by mutations in the __CL