## Abstract Alpha 1 antitrypsin phenotypes and serum levels are presented for a family in which two brothers have Weber Christian disease and ฮฑ1 antitrypsin (PI) Z phenotypes. Clinical histories are described for these two men. A younger brother has the PI Z phenotype but does not have the disease,
Relationship between Weber-Christian panniculitis and the ZZ phenotype of alpha1-antitrypsin
โ Scribed by E. Bleumink; A. H. Klokke
- Publisher
- Springer-Verlag
- Year
- 1985
- Tongue
- English
- Weight
- 175 KB
- Volume
- 277
- Category
- Article
- ISSN
- 0340-3696
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