Pulmonary atresia with intact ventricular septum (PA-IVS) in monozygotic twins
โ Scribed by Danielle De Stefano; Peining Li; Bixia Xiang; Pei Hui; Eduardo Zambrano
- Publisher
- John Wiley and Sons
- Year
- 2008
- Tongue
- English
- Weight
- 268 KB
- Volume
- 146A
- Category
- Article
- ISSN
- 1552-4825
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๐ SIMILAR VOLUMES
## Abstract Cardiac catheterization is infrequently required in babies with pulmonary atresia with intact ventricular septum. The main indications are to decide on the best form of treatment, the options being determined by the right ventricular as well as infundibular morphology and the presence o
Pulmonary atresia with intact ventricular septum (PA/IVS) is a rare disease, accounting for less than 3% of all congenital heart lesions. The cause of PA/IVS is unknown. We report the occurrence of two first cousins with PA/IVS, suggestive of autosomal dominant inheritance with incomplete penetrance
This report describes a 1-day-old infant with valvar pulmonary atresia with intact ventricular septum in whom we were successful in performing transcatheter guidewire perforation and balloon pulmonary valvuloplasty to establish right ventricle-to-pulmonary artery continuity and flow. Also described