This report describes a 1-day-old infant with valvar pulmonary atresia with intact ventricular septum in whom we were successful in performing transcatheter guidewire perforation and balloon pulmonary valvuloplasty to establish right ventricle-to-pulmonary artery continuity and flow. Also described
Catheterization in neonates with pulmonary atresia with intact ventricular septum
β Scribed by Shakeel A. Qureshi
- Publisher
- John Wiley and Sons
- Year
- 2006
- Tongue
- English
- Weight
- 261 KB
- Volume
- 67
- Category
- Article
- ISSN
- 1522-1946
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β¦ Synopsis
Abstract
Cardiac catheterization is infrequently required in babies with pulmonary atresia with intact ventricular septum. The main indications are to decide on the best form of treatment, the options being determined by the right ventricular as well as infundibular morphology and the presence of rightβventricle dependent coronary circulation. In most cases, an interventional approach is appropriate. This can consist of radiofrequency or laser perforation of the atretic pulmonary valve, combined with balloon dilation. In some patients, additional stenting of the arterial duct may be needed.Β© 2006 WileyβLiss, Inc.
π SIMILAR VOLUMES
Pulmonary atresia with intact ventricular septum (PA/IVS) is a rare disease, accounting for less than 3% of all congenital heart lesions. The cause of PA/IVS is unknown. We report the occurrence of two first cousins with PA/IVS, suggestive of autosomal dominant inheritance with incomplete penetrance