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Pregnancy and paroxysmal nocturnal hemoglobinuria

โœ Scribed by Joke Bais; Maria Pel; Albert von dem Borne; Hans van der Lelie


Book ID
118952655
Publisher
Elsevier Science
Year
1994
Tongue
English
Weight
383 KB
Volume
53
Category
Article
ISSN
0301-2115

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Paroxysmal nocturnal hemoglobinuria (PNH) is a rare clonal stem-cell disorder in which blood cells lack complement inhibiting membrane proteins, and become susceptible to complement-mediated injury, leading to chronic intravascular hemolysis and pancytopenia. Glucocorticoids have been a mainstay of