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Pathogenetic mechanisms of fetal akinesia deformation sequence and oligohydramnios sequence

✍ Scribed by Rodríguez, José Ignacio ;Palacios, José

Book ID
102702643
Publisher
John Wiley and Sons
Year
1991
Tongue
English
Weight
709 KB
Volume
40
Category
Article
ISSN
0148-7299

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✦ Synopsis

Abstract

This article briefly reviews the participation of fetal compression, muscular weakness, and fetal akinesia in the genesis of the anomalies found in fetal akinesia deformation sequence (FADS) and oligohydramnios sequence (OS). Both sequences share phenotypic manifestations, such as arthrogryposis, short umbilical cord, and lung hypoplasia, in relation to decreased intrauterine fetal motility. Other characteristic manifestations found in OS, such as Potter face, and redundant skin, are produced by fetal compression. On the other hand, growth retardation, craniofacial anomalies, micrognathia, long bone hypoplasia, and polyhydramnios found in FADS could be related to intrauterine muscular weakness.

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