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Paroxysmal Nocturnal Hemoglobinuria Superimposed with Preeclampsia

✍ Scribed by Mann-Ling Chen; Chen-Hsiang Yu; Fong-Ming Chang; Pao-Lin Kuo


Book ID
117697312
Publisher
Elsevier Science
Year
2006
Tongue
English
Weight
55 KB
Volume
45
Category
Article
ISSN
1028-4559

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Paroxysmal nocturnal hemoglobinuria (PNH) is a rare clonal stem-cell disorder in which blood cells lack complement inhibiting membrane proteins, and become susceptible to complement-mediated injury, leading to chronic intravascular hemolysis and pancytopenia. Glucocorticoids have been a mainstay of