𝔖 Bobbio Scriptorium
✦   LIBER   ✦

Eosinophilic fasciitis with paroxysmal nocturnal hemoglobinuria

✍ Scribed by de Boysson, Hubert; Chèze, Stéphane; Chapon, Françoise; Le Mauff, Brigitte; Auzary, Christophe; Geffray, Loïk


Book ID
123186137
Publisher
Elsevier Science
Year
2013
Tongue
English
Weight
404 KB
Volume
80
Category
Article
ISSN
1297-319X

No coin nor oath required. For personal study only.


📜 SIMILAR VOLUMES


Paroxysmal Nocturnal Hemoglobinuria
✍ Mitsuhiro Omine; Taroh Kinoshita; Hideki Nakakuma; Jaroslaw P.Maciejewski; Charl 📂 Article 📅 2005 🏛 Carden Jennings Publishing 🌐 English ⚖ 185 KB
Danazol for paroxysmal nocturnal hemoglo
✍ Harrington, William J.; Kolodny, Luciano; Horstman, Lawrence L.; Jy, Wenche; Ahn 📂 Article 📅 1997 🏛 John Wiley and Sons 🌐 English ⚖ 45 KB

Paroxysmal nocturnal hemoglobinuria (PNH) is a rare clonal stem-cell disorder in which blood cells lack complement inhibiting membrane proteins, and become susceptible to complement-mediated injury, leading to chronic intravascular hemolysis and pancytopenia. Glucocorticoids have been a mainstay of