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Osteopathia striata, cranial sclerosis with cleft palate and facial nerve palsy

✍ Scribed by L. Kornreich; M. Grunebaum; N. Ziv; A. Shuper; M. Mimouni

Publisher
Springer
Year
1988
Tongue
English
Weight
788 KB
Volume
147
Category
Article
ISSN
0340-6997

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✦ Synopsis

Osteopathia striata (OS) is a rare bone dysplasia characterized by longitudinal sclerotic striations of the long bones. It is of no clinical importance, but OS associated with cranial sclerosis represents a separate entity with a high incidence of palatine malformations and deafness. Only 19 cases of this entity have been reported in the literature. One patient of this series also had facial nerve paralysis. This paper presents a second case of O S, cranial sclerosis, palatine pathology and recurrent facial nerve paralysis. This incidence of 2/20 (10%) does not seem to be coincidental but raises the possibility that facial nerve palsy is one of the clinical manifestations of this specific bone abnormality.

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