Orbital rhabdomyosarcoma in a three week old infant

✍ Scribed by Laila L. Basta; Edward J. DePersio; Ross E. Brown

• Publisher: John Wiley and Sons
• Year: 1976
• Tongue: English
• Weight: 251 KB
• Volume: 4
• Category: Article
• ISSN: 0091-2751
• DOI: 10.1002/jcu.1870040310

✦ Synopsis

Rhabdomyosarcoma is the most caixnon primary malignant orbital tumor in infants and children (1 -3). The increasing recognition of this tumor is probably due to an actual increase in incidence (2), as well as to increased diagnostic acumen of ophthalmic surgeons and opthalmic pathologists.

We are reporting a three week old infant in whom eye examination using ultrasound techniques proved of substantial value in assessing the effect of radiotherapy in the management of orbital rhabdomyosarcoma. CASE REPORT A three week old white infant presented in November 1974 with a swollen right eye and the diagnosis of an orbital tumor was made. Part of the tumor was removed surgically and a biopsy was sent for examination. Pathologic study revealed embryonal rhabdomyosarcoma. The patient was transferred to the Children's Memorial Hospital of the University of Oklahoma Health Sciences Center for further evaluation and definitive treatment.

The patient was the offspring of an uncomplicated pregnancy and there was no family history of cancer. Physical examination showed a welldeveloped, well-nourished, white male in no acute distress. There was no evidence of regional lymph node involvement nor of distant metatatic disease.

The right eye was markedly proptotic, with gross edema and discoloration of both eyelids ~~~m t h e