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Muscle cells and motoneurons differentially remove mutant SOD1 causing familial amyotrophic lateral sclerosis

✍ Scribed by Elisa Onesto; Paola Rusmini; Valeria Crippa; Nicola Ferri; Arianna Zito; Mariarita Galbiati; Angelo Poletti

Book ID: 111184512
Publisher: John Wiley and Sons
Year: 2011
Tongue: English
Weight: 885 KB
Volume: 118
Category: Article
ISSN: 0022-3042
DOI: 10.1111/j.1471-4159.2011.07298.x

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## Abstract Amyotrophic lateral sclerosis (ALS) is the most common fatal motor neuron disease, affecting mostly middle‐aged people. There are no curative therapies for ALS. Several lines of evidence have supported the notion that the proapoptotic property of familial ALS (FALS)‐linked mutant Cu/Zn‐