𝔖 Bobbio Scriptorium

✦ LIBER ✦

Mechanism of toxicity of the branched-chain fatty acid phytanic acid, a marker of Refsum disease, in astrocytes involves mitochondrial impairment

✍ Scribed by Georg Reiser; Peter Schönfeld; Stefan Kahlert

Book ID: 116551388
Publisher: Elsevier Science
Year: 2006
Tongue: English
Weight: 496 KB
Volume: 24
Category: Article
ISSN: 0736-5748
DOI: 10.1016/j.ijdevneu.2005.11.002

No coin nor oath required. For personal study only.

📜 SIMILAR VOLUMES

The Refsum disease marker phytanic acid,

The Refsum disease marker phytanic acid, a branched chain fatty acid, affects Ca2+ homeostasis and mitochondria, and reduces cell viability in rat hippocampal astrocytes

✍ Stefan Kahlert; Peter Schönfeld; Georg Reiser 📂 Article 📅 2005 🏛 Elsevier Science 🌐 English ⚖ 446 KB

The influence of the branched-chain fatt

The influence of the branched-chain fatty acids pristanic acid and Refsum disease-associated phytanic acid on mitochondrial functions and calcium regulation of hippocampal neurons, astrocytes, and oligodendrocytes

✍ Sabine Rönicke; Nicol Kruska; Stefan Kahlert; Georg Reiser 📂 Article 📅 2009 🏛 Elsevier Science 🌐 English ⚖ 900 KB

The existence of an alternative pathway

The existence of an alternative pathway for the degradation of branch-chained fatty acids, and its failure in heredopathia atactica polyneuriti-formis (Refsum's disease)

✍ Lorentz Eldjarn; Kenneth Try; Oddvar Stokke 📂 Article 📅 1966 🏛 Elsevier Science 🌐 English ⚖ 221 KB

Marked inhibition of Na+, K+- ATPase act

Marked inhibition of Na+, K+- ATPase activity and the respiratory chain by phytanic acid in cerebellum from young rats: possible underlying mechanisms of cerebellar ataxia in Refsum disease

✍ Estela Natacha Brandt Busanello… 📂 Article 📅 2012 🏛 Springer US 🌐 English ⚖ 200 KB

1645. Refsum and α-oxidation: Stokke, O.

1645. Refsum and α-oxidation: Stokke, O., Try, K. & Eldjarn, L. (1967), α-Oxidation as an alternative pathway for the degradation of branched-chain fatty acids in man, and its failure in patients with Refsum's disease. Biochim. Biophys. Acta144, 271

📂 Article 📅 1968 🏛 Elsevier Science ⚖ 147 KB

1021. More about Refsum's disease: Eldja

1021. More about Refsum's disease: Eldjarn, L. (1965). Heredopathia atactica polyneuritiformis (Refsum's disease)—A defect in the omega-oxidation mechanism of fatty acids. Scand. J. clin. Lab. Invest. 17, 178. Kolodny, E. H., Hass, W. K., Lane, B. & Drucker, W. D. (1965). Refsum's syndrome. Report of a case including electron microscopic studies of the liver. Archs Neurol., Chicago 12, 583

📂 Article 📅 1966 🏛 Elsevier Science ⚖ 166 KB