Malignant schwannoma of “triton” tumor type

✍ Scribed by D'angio, Giulio J. ;Raney, R. Beverly

• Publisher: John Wiley and Sons
• Year: 1978
• Tongue: English
• Weight: 287 KB
• Volume: 5
• Category: Article
• ISSN: 0098-1532
• DOI: 10.1002/mpo.2950050116

✦ Synopsis

The patient is a seven-year-old boy who was apparently healthy until Thanksgiving 1976 when he went to get fitted for a new pair of pants and was found to have a huge lesion in the left upper medial thigh, which neither he nor his parents had previously noted. The surgeon at another institution removed an apparently completely encapsulated 8 X 8 X 10 cm mass from the deep tissue around the adductor muscles of the thigh. The mass was adjacent and adherent to the sciatic nerve and may have derived directly from the sciatic nerve itself. He had a local excision of this tumor, which was apparently completely removed except for a tag of capsule at the junction between the sciatic nerve and the tumor capsule itself. He was then referred to this hospital for further diagnosis and work-up for metastatic disease. At that time, the diagnosis of fibrosarcoma was made from permanent sections of the tumor, large scar in the area of resection. Thbe was no clinical evidence or definite family history of neurofibromatosis or caf6-au-lait spots.

When he came here, his physical examination was normal except for a well-healed RADIOLOGIC STUDIES: Dr. Gerald Mandell (Pediatric Raditalogist) Multiple films were obtained and no bony or soft-tissue abnormalities were shown. There were no bony evidences of neurofibromatosis, such as dysplastic areas of bone which are sometimes highly suggestive of underlying neurofibromatosis. Liver scans were normal without evidence of enlargement. The lung fields were clear with no evidence of metastatic disease.