✦ LIBER ✦

Immunocytochemistry of muscle cytoskeletal proteins in acid maltase deficiency

✍ Scribed by Dr. Giuseppe Vita; Dr. Alba Migliorato; Dr. Antonio Toscano; Dr. Andreina Bordoni; Dr. Nereo Bresolin; Dr. Agata Fiumara; Dr. Corrado Messina

Publisher: John Wiley and Sons
Year: 1994
Tongue: English
Weight: 643 KB
Volume: 17
Category: Article
ISSN: 0148-639X
DOI: 10.1002/mus.880170614

No coin nor oath required. For personal study only.

📜 SIMILAR VOLUMES

Muscle computed tomography in adult-onse

Muscle computed tomography in adult-onset acid maltase deficiency

✍ Aeiko E.J. de Jager; Ton M. van der Vliet; Taco C. van der Ree; Bart J. Oosterin 📂 Article 📅 1998 🏛 John Wiley and Sons 🌐 English ⚖ 85 KB

Nine patients with adult-onset acid maltase deficiency (Pompe's disease) were examined clinically and with computed tomography (CT). The CT scan showed early and severe involvement of the muscles of trunk and thighs, with selective sparing of the tensor fasciae latae, short head of biceps femoris, g

Respiratory improvement by muscle traini

Respiratory improvement by muscle training in adult-onset acid maltase deficiency

✍ Dr. Richard J. Martin; Dr. Robert L. Sufit; Dr. Steven P. Ringel; Dr. David W. H 📂 Article 📅 1983 🏛 John Wiley and Sons 🌐 English ⚖ 240 KB

## Abstract A patient with progressive involvement of respiratory function from adult‐onset acid maltase deficiency is reported. The decrement in objective and subjective waking and sleeping respiratory variables was significantly reversed by inspiratory muscle training. This training was accomplis

Qualitative and quantitative skeletal mu

Qualitative and quantitative skeletal muscle ultrasound in late-onset acid maltase deficiency

✍ Craig M. Zaidman; Elizabeth C. Malkus; Catherine Siener; Julaine Florence; Alan 📂 Article 📅 2011 🏛 John Wiley and Sons 🌐 English ⚖ 290 KB

α-Glucosidase isoenzymes in normal and a

α-Glucosidase isoenzymes in normal and acid maltase-deficient human skeletal muscles

✍ Fusako Usuki; Shoichi Ishiura; Ikuya Nonaka; Dr. Hideo Sugita 📂 Article 📅 1988 🏛 John Wiley and Sons 🌐 English ⚖ 565 KB

Developmental study of α-glucosidases in

Developmental study of α-glucosidases in japanese quails with acid maltase deficiency

✍ Fusako Usuki; Shoichi Ishiura; Dr. Hideo Sugita 📂 Article 📅 1986 🏛 John Wiley and Sons 🌐 English ⚖ 516 KB

In Japanese quails with late-onset acid maltase deficiency (AMD), the activity of acid a-glucosidase was severely reduced to approximately 16% of the normal level from an embryonic age. The kinetic characteristics and inhibition by Zn indicated that the residual activity was responsible for the intr

Location of and post-mortem changes in s

Location of and post-mortem changes in some cytoskeletal proteins in pork and cod muscle

✍ Morrison, E Heather; Bremner, H Allan; Purslow, Peter P 📂 Article 📅 2000 🏛 John Wiley and Sons 🌐 English ⚖ 482 KB

The cytoskeletal proteins actin, nebulin, spectrin, desmin, vinculin and talin were labelled immunohistochemically in sections of muscle from commercially available pigs and cod (Gadus morhua) taken pre-rigor and from samples stored for several days. Actin, nebulin and spectrin gave similar labellin