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Enhanced GM1 ganglioside catabolism in cultured fibroblasts from Alzheimer patients

โœ Scribed by Marina Pitto; Francesca Raimondo; Chiara Zoia; Laura Brighina; Carlo Ferrarese; Massimo Masserini


Book ID
116780547
Publisher
Elsevier Science
Year
2005
Tongue
English
Weight
106 KB
Volume
26
Category
Article
ISSN
0197-4580

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GM1-gangliosidosis: Accumulation of gang
โœ Yoshiyuki Suzuki; Norimasa Nakamura; Kazuko Fukuoka ๐Ÿ“‚ Article ๐Ÿ“… 1978 ๐Ÿ› Springer ๐ŸŒ English โš– 270 KB

Uptake of radioactivity from 14C-galactose into gangliosides by cultured skin fibroblasts was studied. GM3 was the major ganglioside in control human fibroblasts. An increase of GM1 was demonstrated in GM1-gangliosidosis fibroblasts. The degree of GM1 accumulation was correlated with the clinical ty