We describe a 16-year-old girl with systemic-onset juvenile arthritis who presented with pulmonary hypertension, without evidence of pleural or parenchymal involvement of the lung, pulmonary vasculitis, or immune deposition in the pulmonary vasculature. Pleuropulmonary involvement occurs occasionall
Echocardiographic findings in a patient with primary pulmonary hypertension
β Scribed by Lense, Lloyd D. ;Kronzon, Itzhak ;Danilowicz, Delores ;Schloss, Michael ;Singh, Amarjit
- Publisher
- John Wiley and Sons
- Year
- 1976
- Tongue
- English
- Weight
- 533 KB
- Volume
- 2
- Category
- Article
- ISSN
- 0098-6569
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β¦ Synopsis
Abstract
This is a report of the echocardiographic findings in a 9βyearβold white female with primary pulmonary arterial hypertension confirmed by catheterization and later at autopsy. The reported findings of an absent βaβ wave, a flat diastolic E to F slope, and a midsystolic closure of the pulmonic valve were observed. In addition, tricuspid valve prolapse was noted. Prolapse of the tricuspid valve may be part of the mechanism of tricuspid insufficiency in a patient with pulmonary hypertension.
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