✦ LIBER ✦

Primary Pulmonary Hypertension: An Unusual Case Associated with Extrahepatic Portal Hypertension

✍ Scribed by Mark D. Cohen; Lewis J. Rubin; Wayne E. Taylor; Jennifer A. Cuthbert

Publisher: John Wiley and Sons
Year: 2007
Tongue: English
Weight: 616 KB
Volume: 3
Category: Article
ISSN: 0270-9139
DOI: 10.1002/hep.1840030419

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✦ Synopsis

A patient with both extrahepatic portal hypertension and primary pulmonary hypertension is reported. The pulmonary hypertension developed without a surgical portal-systemic shunt, and at autopsy there was no evidence of a large spontaneous shunt. This association of pulmonary arterial hypertension and portal venous hypertension without either intrinsic liver disease or a large portal-systemic anastomosis has not been reported previously. Our case supports the concept that portal hypertension with its attendant portal-systemic collateral circulation may be the major predisposing cause of pulmonary hypertension both in intrinsic liver disease and extrahepatic portal vein obstruction.

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