✦ LIBER ✦

Correlations between branched-chain amino acids and branched-chain α-keto acids in blood in maple syrup urine disease

✍ Scribed by U. Langenbeck; U. Wendel; Angelika Mench-Hoinowski; D. Kuschel; K. Becker; Hildegard Przyrembel; H.J. Bremer

Book ID: 115822372
Publisher: Elsevier Science
Year: 1978
Tongue: English
Weight: 697 KB
Volume: 88
Category: Article
ISSN: 0009-8981
DOI: 10.1016/0009-8981(78)90433-3

No coin nor oath required. For personal study only.

📜 SIMILAR VOLUMES

Peritoneal dialysis in maple-syrup-urine

Peritoneal dialysis in maple-syrup-urine disease: Studies on branched-chain amino and keto acids

✍ U. Wendel; K. Becker; Hildegard Przyrembel; Monika Bulla; C. Manegold; Angelika 📂 Article 📅 1980 🏛 Springer 🌐 English ⚖ 562 KB

Elevated excretion of N-acetylated branc

Elevated excretion of N-acetylated branched-chain amino acids in maple syrup urine disease

✍ W. Lehnert; E. Werle 📂 Article 📅 1988 🏛 Elsevier Science 🌐 English ⚖ 256 KB

Renal clearance of branched-chain L-amin

Renal clearance of branched-chain L-amino and 2-oxo acids in maple syrup urine disease

✍ P. Schadewaldt; H.-W. Hammen>; A.-C. Ott; U. Wendel 📂 Article 📅 1999 🏛 Springer 🌐 English ⚖ 164 KB

Branched-chain alpha-keto acids isolated

Branched-chain alpha-keto acids isolated as oxime derivatives: Relationship to the corresponding hydroxy acids and amino acids in Maple Syrup Urine Disease

✍ Gerald Lancaster; Orval A. Mamer; Charles R. Scriver 📂 Article 📅 1974 🏛 Elsevier Science 🌐 English ⚖ 703 KB

Maple syrup urine disease: Branched-chai

Maple syrup urine disease: Branched-chain amino acid concentrations and metabolism in cultured human lymphoblasts

✍ Stephen D. Skaper; Daniel P. Molden; J. Edwin Seegmiller 📂 Article 📅 1976 🏛 Springer 🌐 English ⚖ 707 KB

The intracellular concentration of free leucine, isoleucine, and valine and their metabolism were studied in lymphoblast cultures established from peripheral blood of an individual with maple syrup urine disease (MSUD) and a control subject. Branched-chain alpha-keto acid decarboxylase activity in t

Branched-Chain α-Keto Acids Accumulating

Branched-Chain α-Keto Acids Accumulating in Maple Syrup Urine Disease Induce Reorganization of Phosphorylated GFAP in C6-Glioma Cells

✍ Cláudia Funchal; André Quincozes Santos; Maria Caroline Jacques-Silva; Ariane Za 📂 Article 📅 2005 🏛 Springer 🌐 English ⚖ 477 KB