## Abstract Severe neurological symptoms, cerebral edema, and atrophy are common features of the inherited metabolic disorder maple syrup urine disease (MSUD). However, the pathomechanisms involved in the neuropathology of this disease are not well established. In this study, we investigated the ef
✦ LIBER ✦
Branched-Chain α-Keto Acids Accumulating in Maple Syrup Urine Disease Induce Reorganization of Phosphorylated GFAP in C6-Glioma Cells
✍ Scribed by Cláudia Funchal; André Quincozes Santos; Maria Caroline Jacques-Silva; Ariane Zamoner; Carmem Gottfried; Moacir Wajner; Regina Pessoa-Pureur
- Publisher
- Springer
- Year
- 2005
- Tongue
- English
- Weight
- 477 KB
- Volume
- 20
- Category
- Article
- ISSN
- 0885-7490
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