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Clinical measures of dysarthria in Friedreich Ataxia

โœ Scribed by Arunjot Singh; Elizabeth Epstein; Lauren M. Myers; Jennifer M. Farmer; David R. Lynch

Publisher
John Wiley and Sons
Year
2009
Tongue
English
Weight
437 KB
Volume
25
Category
Article
ISSN
0885-3185

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โœฆ Synopsis

Abstract

Dysarthria in Friedreich Ataxia (FA) is difficult to quantify. This study evaluated a series of performance measures for speech in 22 patients with genetically confirmed FA and 16 ageโ€matched controls. Tests included the PATA examination, the PATAKA examination, the Oral Motor component of the Boston Aphasia examination, the Boston Cookie Theft description task, and the Assessment of Intelligibility of Dysarthric Speech. All measures, except the Cookie theft description task, demonstrated significantly lower scores for patients with FA when compared with controls and correlated with measures of disease progression. Thus, four of five measures capture speech dysfunction in FA and may provide feasible, inexpensive, quantitative testing for therapeutic monitoring in FA. ยฉ 2009 Movement Disorder Society

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