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Clinical and Molecular Heterogeneity of δ, β-Thalassemia in Sicily

✍ Scribed by GINO SCHILIRÓ; SALVATORE MUSUMECI; MARIA ANTONIETTA ROMEO; FELICIA DI GREGORIO; ALFONSINA D'AGATA; ROSARIO TESTA; GIUSEPPE RUSSO


Book ID
118722352
Publisher
John Wiley and Sons
Year
1985
Tongue
English
Weight
395 KB
Volume
445
Category
Article
ISSN
0890-6564

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Heterogeneity in β0thalassemia from Alge
✍ Mériem Belhani; F. Morlé; P. Colonna; Jacqueline Godet 📂 Article 📅 1980 🏛 Springer 🌐 English ⚖ 537 KB

Six Algerian patients with beta 0 thalassemia are presented, in addition to the two patients already reported (Godet et al., 1977). Family studies indicate that all the patients had homozygous beta thalassemia characterized by absence of beta globin chain synthesis in peripheral blood. The clinical