Severe liver disease is an unusual but potentially fatal complication of sickle-cell disease (SCD). Liver transplantation has been complicated by ongoing SCD and thrombosis. We reviewed 214 pediatric transplants done at our institution from 1990 to 2005. Three patients were transplanted for complica
Cholecystosonography in children with sickle cell disease: Technical approach and clinical results
β Scribed by Jerome J. Cunningham; Stephen M. Houlihan; C. Altay
- Publisher
- John Wiley and Sons
- Year
- 1981
- Tongue
- English
- Weight
- 476 KB
- Volume
- 9
- Category
- Article
- ISSN
- 0091-2751
No coin nor oath required. For personal study only.
β¦ Synopsis
Abstract
Fortyβfive children with sickle cell anemia were studied with meticulous cholecystosonograms using a 5βMHz thyroid transducer. Goodβquality images were obtained. The most informative and useful view was the leftβsideβdown decubitus study with the ultrasound gantry angled 45% to the anteroposterior axis. Rotating the patient rapidly through 360 degrees did not increase the information content of the examination. We found that one third of a random group of children with sickle cell anemia will have gallstones and one fifth will have βsludgeβ. A kinked deformity of the gallbladder may simulate a gallstone. Neither age, sex, weight, physical findings (except for hepatomegaly), nor a variety of biochemical measurements of the blood will be of much value in predicting gallbladder disease in any given patient.
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