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Arrhythmogenic right ventricular dysplasia/cardiomyopathy

โœ Scribed by Victor A. Ferrari; Craig H. Scott; Cristina Basso


Book ID
107535062
Publisher
Springer
Year
2005
Tongue
English
Weight
265 KB
Volume
7
Category
Article
ISSN
1523-3782

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Arrhythmogenic right ventricular dysplasia/ cardiomyopathy (ARVD/C) is a hereditary cardiomyopathy characterized by fibrofatty replacement of cardiomyocytes, ventricular tachyarrhythmias and sudden death. ARVD/C is mainly caused by mutations in genes encoding desmosomal proteins. However, the pathog