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Arrhythmogenic right ventricular dysplasia/ cardiomyopathy

โœ Scribed by Kalpana R. Prakasa; Hugh Calkins


Book ID
107555716
Publisher
Springer
Year
2005
Tongue
English
Weight
379 KB
Volume
7
Category
Article
ISSN
1092-8464

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Arrhythmogenic right ventricular dysplasia/ cardiomyopathy (ARVD/C) is a hereditary cardiomyopathy characterized by fibrofatty replacement of cardiomyocytes, ventricular tachyarrhythmias and sudden death. ARVD/C is mainly caused by mutations in genes encoding desmosomal proteins. However, the pathog