An 18-month-old female presented with an abdominal tumor mass which on morphological, immunohistological and ultrastructural examination was found to be a malignant fibrous histiocytoma. This soft tissue sarcoma is rarely encountered in childhood. Treatment in this case consisted of surgical tumor d
Angiomatoid (malignant) fibrous histiocytoma as a second tumour in a child with neuroblastoma
β Scribed by C. Gambini; R. Haupt; F. Rongioletti
- Publisher
- John Wiley and Sons
- Year
- 2000
- Tongue
- English
- Weight
- 278 KB
- Volume
- 142
- Category
- Article
- ISSN
- 0007-0963
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β¦ Synopsis
Abstract
Neuroblastoma occurring as a disseminated disease in children has a poor prognosis. Haematogenous metastases usually involve the marrow, bone, liver and skin. A second neoplasm may also develop. We describe a child with retroperitoneal neuroblastoma (stage 3) who developed a nodular mass in the inguinal area which was suspected to be a metastasis. Histopathology disclosed an angiomatoid (malignant) fibrous histiocytoma, and excision was curative. The occurrence of angiomatoid (malignant) fibrous histiocytoma as a second tumour in a patient with neuroblastoma has not previously been reported.
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