Sickle cell anemia and the related hemoglobinopathies are associated with a large spectrum of renal abnormalities. The patients have impaired urinary concentrating ability, defects in urinary acidification and potassium excretion, and supranormal proximal tubular function. The latter is manifest by
Anaesthesia for renal transplantation in sickle cell disease
β Scribed by Henry K. Gyasi; A. W. Zarroug; M. Matthew; R. Joshi; A. Daar
- Publisher
- Springer-Verlag
- Year
- 1990
- Tongue
- French
- Weight
- 667 KB
- Volume
- 37
- Category
- Article
- ISSN
- 1496-8975
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Severe liver disease is an unusual but potentially fatal complication of sickle-cell disease (SCD). Liver transplantation has been complicated by ongoing SCD and thrombosis. We reviewed 214 pediatric transplants done at our institution from 1990 to 2005. Three patients were transplanted for complica
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