An Infant with Kasabach-Merritt Syndrome with Associated Renal Hematoma and Intussusception
โ Scribed by Guthrie, Scott O; Rhodes, Melissa; Janco, Robert; Stein, Sharon M; Jabs, Kathy; Engelhardt, Barbara
- Book ID
- 110051941
- Publisher
- Nature Publishing Group
- Year
- 2005
- Tongue
- English
- Weight
- 108 KB
- Volume
- 25
- Category
- Article
- ISSN
- 1300-5251
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๐ SIMILAR VOLUMES
A two-month-old infant developed a vascular tumor of the right flank which, upon biopsy, proved to be a spindle cell hemangioendothelioma. The increased capillary bed characterizing the neoplasm caused a severe thrombocytopenia together with a consumption coagulopathy (Kasabach-Merritt syndrome). Th
Kasabach-Merritt syndrome (KMS) is a severe vascular growth disorder associated with generalized kaposiform hemangioendotheliomas, tufted angiomas, consumptive coagulopathy, and thrombocytopenia. [1][2][3] Since the initial report, 1 case series have addressed its complex pathophysiology and treatme