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Abnormal auditory evoked potentials in hereditary motor-sensory neuropathy

✍ Scribed by Dr Saty Satya-Murti; Anthony T. Cacace; Peggy A. Hanson

Publisher: John Wiley and Sons
Year: 1979
Tongue: English
Weight: 327 KB
Volume: 5
Category: Article
ISSN: 0364-5134
DOI: 10.1002/ana.410050506

No coin nor oath required. For personal study only.

✦ Synopsis

Abstract

From a kinship with a dominantly inherited motor‐sensory neuropathy, we studied 2 brothers with brainstem auditory evoked potentials and behavioral audiometric tests. They had abnormal prolongation of I‐III interpeak intervals. Wave V was poorly developed. Conventional audiometric tests did not reveal a peripheral hearing loss. It is probable that their auditory nerves and spiral ganglia are undergoing a pathophysiological process analogous to that of their peripheral nerves.

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