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Focal posterior interosseous neuropathy in the presence of hereditary motor and sensory neuropathy, type I

✍ Scribed by Gregory T. Carter; David D. Kilmer; Robert M. Szabo; Craig M. McDonald

Publisher
John Wiley and Sons
Year
1996
Tongue
English
Weight
484 KB
Volume
19
Category
Article
ISSN
0148-639X

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✦ Synopsis

A 30-year-old male with hereditary motor and sensory neuropathy, type I (HMSN I), presented with asymmetric weakness of finger extension and radial deviation with left wrist extension, previously felt to be a manifestation of the peripheral neuropathy. Nerve conduction studies confirmed HMSN I; however, needle EMG revealed marked, ongoing axonal loss in muscles innervated by the left posterior interosseous nerve (PIN) only. At surgery there was focal fusiform swelling in the PIN at exit from the supinator muscle, compatible with localized hypertrophic neuropathy, which has not been reported before in HMSN I. A concomitant focal mononeuropathy should be considered in cases of hereditary neuropathy with marked asymmetry of weakness. 0

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