Electromyogram and nerve conduction in p
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K. A. FlΓΌgel; K.-F. Druschky
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Article
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1977
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Springer
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English
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Diminished activity of uroporphyrinogen I-synthetase in the liver and other tissues may be regarded to be the primary genetic deficiency of acute intermittent porphyria (AIP). Increased production and renal excretion of delta-aminolevulinic acid (ALA) und porphobilinogen (PBG) are secondary phenomen