✦ LIBER ✦

β-Galactosidase-deficient mouse as an animal model for GM1-gangliosidosis

✍ Scribed by Junichiro Matsuda; Osamu Suzuki; Akihiro Oshima; Atsuo Ogura; Yoko Noguchi; Yoshie Yamamoto; Toshihiko Asano; Kazuhiro Takimoto; Kazuko Sukegawa; Yoshiyuki Suzuki; Masaharu Naiki

Book ID: 110372853
Publisher: Springer US
Year: 1997
Tongue: English
Weight: 806 KB
Volume: 14
Category: Article
ISSN: 1573-4986
DOI: 10.1023/a:1018573518127

No coin nor oath required. For personal study only.

📜 SIMILAR VOLUMES

Insights into post-translational process

Insights into post-translational processing of β-galactosidase in an animal model resembling late infantile human GM1-gangliosidosis

✍ R. Kreutzer; M. Kreutzer; M. J. Pröpsting; A. C. Sewell; T. Leeb; H. Y. Naim; W. 📂 Article 📅 2008 🏛 Carol Davila University of Medicine Bucharest, Rom 🌐 English ⚖ 467 KB

Characterisation of the oldest inbred mo

Characterisation of the oldest inbred mouse strain, DBA/2j, as a bona fide adult onset model of GM1 gangliosidosis caused by mis-localisation of β-galactosidase

✍ Lloyd-Evans, Emyr; Walker, Mathew 📂 Article 📅 2014 🏛 Elsevier Science 🌐 English ⚖ 42 KB

1-Deoxy-d-galactonojirimycins with dansy

1-Deoxy-d-galactonojirimycins with dansyl capped N-substituents as β-galactosidase inhibitors and potential probes for GM1 gangliosidosis affected cell lines

✍ Richard F.G. Fröhlich; Richard H. Furneaux; Don J. Mahuran; Robert Saf; Arnold E 📂 Article 📅 2011 🏛 Elsevier Science 🌐 English ⚖ 598 KB

Trimellitic anhydride-sensitive mouse as

Trimellitic anhydride-sensitive mouse as an animal model for contact urticaria

✍ Antti I. Lauerma; Benson Fenn; Howard I. Maibach 📂 Article 📅 1997 🏛 John Wiley and Sons 🌐 English ⚖ 57 KB

Key words: trimellitic anhydride; contact urticaria

Transgenic mouse expressing human mutant

Transgenic mouse expressing human mutant α-galactosidase A in an endogenous enzyme deficient background: a biochemical animal model for studying active-site specific chaperone therapy for Fabry disease

✍ Satoshi Ishii; Hidekatsu Yoshioka; Kazuaki Mannen; Ashok B. Kulkarni; Jian-Qiang 📂 Article 📅 2004 🏛 Elsevier Science 🌐 English ⚖ 237 KB

The BALB/c mouse as an animal model for

The BALB/c mouse as an animal model for progressive sensorineural hearing loss

✍ James F Willott; Jeremy G Turner; Stephanie Carlson; Dalian Ding; Lori Seegers B 📂 Article 📅 1998 🏛 Elsevier Science 🌐 English ⚖ 392 KB