X-linked adrenoleukodystrophy mice demonstrate abnormalities in cholesterol metabolism
✍ Scribed by Isabelle Weinhofer; Sonja Forss-Petter; Markus Kunze; Mihaela Žigman; Johannes Berger
- Book ID
- 116466011
- Publisher
- Elsevier Science
- Year
- 2005
- Tongue
- English
- Weight
- 204 KB
- Volume
- 579
- Category
- Article
- ISSN
- 0014-5793
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X-linked hypophosphatemia is a genetic bone disease in humans and mice. Two closely linked mutations in mice, Hyp and G y , cause low plasma phosphate and a rachitic and osteomalacic bone disease. Because of the controversy as to whether Gy is a good model for X-linked hypophosphatemia, the phenotyp