A neurologically normal 3-year-old girl with Type I Crigler-Najjar syndrome was successfully treated with orthotopic liver transplantation. Preoperative serum bilirubin concentrations as high as 31 mg per dl were not diminished with phenobarbital or phototherapy. Bilirubin fractionation of duodenal
Type II Crigler-Najjar syndrome with intrahepatic cholestasis
β Scribed by Atsushi Kagita; Yukihiko Adachi; Akira Kambe; Toshinori Kamisako; Toshio Yamamoto
- Book ID
- 105543546
- Publisher
- Springer Japan
- Year
- 1994
- Tongue
- English
- Weight
- 666 KB
- Volume
- 29
- Category
- Article
- ISSN
- 0944-1174
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Plasmapheresis has been shown to reduce total and free bilirubin levels in acute exacerbations of Crigler-Najjar syndrome, type I (CNS-TI), but its effectiveness in long-term management has not been reported. An 18-year-old (yo) male with CNS-TI, who required prolonged daily high-intensity photother
## which reliable administration of phototherapy cannot This study represents a multicenter survey on the be guaranteed. (HEPATOLOGY 1996;24:311-315.) management of patients with Crigler-Najjar syndrome (CNS) type 1. The aim of the survey was to find guiding principles for physicians in the care o